(n) a congenital progressive disorder of lipid metabolism having an onset at age 5 and characterized by blindness and dementia and early death, Syn. juvenile amaurotic idiocy
(n) a hereditary disorder of lipid metabolism occurring most frequently in individuals of Jewish descent in eastern Europe; accumulation of lipids in nervous tissue results in death in early childhood, Syn. infantile amaurotic idiocy, Tay-Sachs, Sachs disease
The Collaborative International Dictionary of English (GCIDE) v.0.53 Collaborative International Dictionary (GCIDE)